Abstract: Objective: To analysisthe origin,pathology,clinical characteristics and treatment of patients with primary clear cell carcinoma of the nasocavity(CCCN). Methods: Three patients with CCCN hospitalized in Tianjin cancer hospital from august 1992 to September 2003. All three male patients were pathologically confirmed, and the median age was 60 years old. The most common symptom was nasal obstruction, crescendo intensification, rhinorrhea interrupted emarhinorrhea and the nasopharynx indisposition. All patients were treated with radiotherapy. One patient was treated with radiotherapy alone, another was postoperation and the third one with metastatic carcinoma of bone treated with surgy in combination with radiotherapy and chemotherapy. Results: Two patients were still alive. One patient died of heart and respiratory failure. Conclusions: CCCN is a very rare disease which characteristics is local invasion. The primary tumor grows rapidly and may metastatis through lymph drainage and blood system. The combination treatment of surgery, radiotherapy and chemotherapy is efficiacy.