Abstract: Objective : To analyze the incidence of head and neck neurolimmoma in order to direct future diagnosis and treatment. Methods : From July 1969 to September 2002, 342 cases of patients with head and neck tumor originated from nerve system were treated, which accounted for 58.56% (342/584) of all the cases of human neurolimomma, with 275 cases of following-up. The rate of following-up was 80.41%. Results : The number of cases diagnosed correctly before surgery was 184. The misdiagnosis rate was 33.09% (91/275). 7 cases recurred including 3 malignant tumor. The most susceptible nerves were sympathetic nerve, brachial plexus, and vagus nerve. conclusions : Neurolimmoma mostly occurs in head and neck, which accounts for about 60% of the body. Most of them are benign, only 3 of 275 cases are malignant. Treatment mainly depends on surgery. Malignant tumor is insensitive to chemical treatment and radiation, whose prognosis is bad.