Objective  This study aimed to analyze the histopathological and immunohistological characteristics, biologic behaviors, and prognosis of two cases of recurrent renal epithelioid angiomyolipoma(EAML).

  Methods  Two cases of EAML were identified between July 2002 and August 2012 in our institute. Review of literature, as well as observation and analysis of clinical pathological features, biological behavior, and prognosis, was conducted.

  Results  The two cases involved in this study were both females whose average age was 47.5. The EAML both occurred on the patients' left kidney. Through computed tomography(CT) one of them was found to show non-uniform enhancement. Enhanced CT showed progressive strengthening and slight reduction in size. Partial nephrectomy of the left kidney and radical left nephrectomy were used for treatment. The epithelioid cells were arranged in nests or in sheets; the epithelioid cells were large with round or polygon shape.

  Conclusion  he primary difference between epithelioid AML and classic AML of the kidney is the manifestation of rare biological behaviors of invasive proliferation and histological features of atypical hyperplasia. CT is important in making a definite diagnosis by pathology and immunohistochemistry. Surgery is the main treatment method, and no standard prognosis exists to date.